A rare case report of sirenomelia

  • Dr. Abhishek Kumar General Surgery, Specialist Doctor at Sadar Hospital, Hazaribagh &Visiting Consultant at Vandana Nursing Home, Shivpuri, Hazaribag, Jharkhand, India
  • Dr. Snehlata Specialist Doctor at Sadar Hospital, Hazaribagh &Visiting Consultant at Vandana Nursing Home, Shivpuri, Hazaribag, Jharkhand, India
  • Dr. Manjula Srivastava HOD & Associate Professor, Department of Obstetrics & Gynaecology, HMCH, Hazaribagh, Jharkhand, India
Keywords: Caudal regression syndrome, Mermaid syndrome, Potter's facies, Sirenomelia

Abstract

Mermaid syndrome is a rare congenital fetal anomaly with characteristic feature of complete or partial fusion of lower limbs. Although, this syndrome is incompatible with life due to the association of several congenital defect and malformation. In our case Patient was a 31.3 week. A 1.1 kg, preterm infant of unidentified sex was born, a live born, normally delivered at preterm by a 25-year-old primigravida of lower socioeconomic status. Examination of the baby revealed caudal dysgenesis having apparent fusion of the legs into a single lower limb the most severe form, only a single bone is present,with no indication of legs or feet. There was no identifiable external genitalia and anus. Incidentally the infant died after 45 minutes post birth and we report this case due to their rarity and preterm live birth.

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References

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CITATION
DOI: 10.17511/joog.2019.i05.05
Published: 2019-12-18
How to Cite
Kumar, A., Snehlata, S., & Srivastava, M. (2019). A rare case report of sirenomelia. Obs Gyne Review: Journal of Obstetric and Gynecology, 5(5), 237-240. https://doi.org/10.17511/joog.2019.i05.05
Section
Case Report